Infant wd markd hypotonia of all muscles.
CAUSES
1)Central nervous sys
perinatal asphyxia,neonatal encephalopathy,kernicterus, crbl palsy,intracrnl hmrge,chrmsml anamolies lk Downs ,aminoaciduria
2)SPINAL CORD Anamol
ant hrn cell dis-werding hoffman spinal mus atropy,poliomyelitis
3)PERIPHERAL NERUES
acute polyneuropaty ..cong snsry neuropaty
4)MYONEURAL JUN
neont mystenia grvis,infantle botulism
5)MUSCLES
muscle dystrpy,cong myotonic dstrps,cong myopatis,polymyositis,glyco storg dis
6)MISCELLAN
PEM,rikets,prader willi syn,malab syn,cretinism
DIGNOSIS Clinicaly reltve immobilty,bizzre unusl postures
POSTURE frog leggd posn
on vent susp rag doll posn
MOVEMETS
flabby muscles
SCARRF Sign elbow easly crss midline
HEAD LAG whn pull to sit
TREATMT
manage compli of svre weakness
motor neurotropic agnts &embryonic grafts
gabapentin,rilozule
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